A successful dental management in a child with Cornelia de Lange Syndrome: rare case of Cornelia de Lange Syndrome in child / O sucesso do manejo odontológico em criança com Síndrome Cornelia de Lange: um caso raro da Síndrome Cornelia de Lange em criança

Background: the Cornelia de Lange Syndrome (CDLs) is a rare and complex syndrome characterized, basically, by psychomotor retardation associated with a number of congenital malformations. Aims: this paper reports the case of an 11-year-old female child diagnosed with Cornelia de Lange Syndrome (CdLS) and her successful dental management. Case report: the patient had severe mental retardation, definite negative behavior and the clinical findings included oral and physical changes. The patient's oral hygiene was deficient with the presence of calculus and gingivitis, besides several active caries lesions in permanent and deciduous dental elements. The treatment consisted in guidance for caregivers about oral hygiene and diet, and the dental procedures were performed under general anesthesia. Currently, the patient is accompanied by monthly follow-ups. Conclusions: the lack of knowledge about oral hygiene and cariogenic diets was identified as a one of the reasons for the oral diseases present. Due to the need to care for the other more serious and complex health problems, the oral diseases had evolved faster than usual and thus were difficult to treat and maintain thereafter. Under such conditions, the dentist plays a key role within a multidisciplinary team. From the guidance and knowledge provided in the dental clinic, there was a significant improvement in the life quality of the child and her family

Preparo do paciente pediátrico portador de diabetes e Síndrome de Down para tratamento dentário sob anestesia geral / Managing the diabetic paediatric patient with Down Syndrome for dental treatment under general anaesthesia

O diabetes é uma doença caracterizada pela elevaçäo da glicose no sangue, e pela emissäo freqüente e abudante de urina. Devido a sua natureza imunológica, está associado à diversas outras síndromes, de forma que na avaliaçäo clínica destes pacientes, principalmente naqueles que deveräo ser submedidos à procedimentos cirúrgicos, deve-se incluir sempre investigaçäo para a possibilidade da associaçäo com outras doenças. Dessa forma, o objetivo deste artigo foi relatar o preparo de uma paciente diabética portadora da Síndrome de Down, atendida na Unidade Pediátrica de Pacientes Especiais (UPPE) da Faculdade de Odontologia de uma instituiçäo pública de ensino superior, que foi submetida à tratamento dentário sob anestesia geral

Manifestaçöes orais em crianças portadoras de AIDS / Oral manifestation of the children immunodeficiency virus infection HIV

Este trabalho foi realizado com o objetivo de informar, através de uma revisäo de literatura, ao clínico e em especial ao odontopediatra, sobre as características gerais e principalmente as manifestaçöes clínicas orais da Síndrome da Imunodeficiência Adquirida (AIDS) em crianças